产品货号：
Z13482
中文名称：
CHM抗体
英文名称：
Anti-CHM Antibody
产品规格：
50μl|100μl|150μl
发货周期：
1～3天
产品价格：
询价
| 抗体名称 | Anti-CHM Antibody |
| 指标别名 | CHM;Choroideraemia protein;GGTA;REP1;TCD |
| 克隆性 | Polyclonal |
| 检验物种 | human,mouse,rat |
| 应用范围 | WB,ELISA |
| 基因名称 | CHM |
| 抗体来源 | Rabbit |
| 抗体类型 | IgG |
| 免疫原 | E.coli-derived human CHM recombinant protein (Position:A193-Q380). |
| 实际分子量 | 95KD |
| 成分 | 500μg/mL antibody with PBS，0.02% NaN3,1mg BSA and 50% glycerol. |
| 纯化方式 | Immunogen affinity purified. |
| 浓度 | 500μg/mL |
| 产品形态 | 溶液 |
| 保存条件 | 12 months from date of receipt，-20℃ as supplied.6 months 2 to 8℃ after reconstitution.Avoid repeated freezing and thawing. |
| 背景资料 | Rab escort protein 1 (REP1) also known as rab proteins geranylgeranyltransferase component A 1 is an enzyme that in humans is encoded by the CHM gene.This gene encodes component A of the RAB geranylgeranyl transferase holoenzyme.In the dimeric holoenzyme,this subunit binds unprenylated Rab GTPases and then presents them to the catalytic Rab GGTase subunit for the geranylgeranyl transfer reaction.Rab GTPases need to be geranylgeranyled on either one or two cysteine residues in their C-terminus to localize to the correct intracellular membrane.Mutations in this gene are a cause of choroideremia;also known as tapetochoroidal dystrophy (TCD).This X-linked disease is characterized by progressive dystrophy of the choroid,retinal pigment epithelium and retina.Alternatively spliced transcript variants have been found for this gene. |
| Uniprot ID | P24386 |
| 推荐配套试剂 | Biorab recommends Enhanced Chemiluminescent Kit with anti-Rabbit IgG (ZN1926) for Western blot,and HRP Conjugated anti-Rabbit IgG Super Vision Assay Kit (ZN1865) for IHC(P).*Blocking peptide可以联系我们购买。 |
| 推荐稀释比 | Western blot(WB) 1:500～2000 (ELISA)： 1:100～1000 |
相关搜索：CHM抗体，CHM多抗，Anti-CHM Antibody